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- N-acetylglutamate
- N-acetylglutamate Synthase
Deficiency - Argininosuccinate
Synthase - Acetylglutamate
Kinase - N-
acetyltransferase - N-
Acetyl Glutamine - N-acetylglutamate
Synthetase - N-
Acetyl Cysteine Structure - Carbamyl
- Acetylcysteine
- Urea
Cycle - Malate
Dehydrogenase - acetyl-CoA
- Urea Cycle
Enzymes - N-
Acetyl Amino Acids - Carbamoyl Phosphate Synthetase
1 Deficiency - Glutamine Synthetase
Pathway - Acetylornithine
- Acetylornithine
Aminotransferase - N-acetylglutamate
to Acetyl Glutamyl Phosphate - Cysteine Chemical
Structure - Urea Cycle
Disorder - Monoamine
Neurotransmitter - Carglumic
Acid - Acetyl
Donor - Orotic Acid
Urea Cycle - Arginine
Kinase - Carbamyl
Forte - Nag
Structure - N-
Acetyl Ampa - Nags
Deficiency - Acetylornithine
Transaminase - Urea Cycle Involved
Enzymes - Nitric
Cycle - Glutamate
Deficiency - Ornithine Transcarbamylase
Deficiency - Argininosuccinate
Lyase Deficiency - Glutamate
Nitric Oxide - Arginine Biosynthesis
Pathway - Argininosuccinic Acid
Synthetase Deficiency - Valproate
Hyperammonemia - Acetyllactosamine
- Methylglutaconic
Aciduria - Hyperammonia
From Valproate - Acetylcholine Synthesis
Pathway - Acetylglutamate
Semialdehyde - 3-Methylglutaconic Aciduria
- Cysteine HCL
Monohydrate - 2-Acetoxybenzoic Acid
- Ammonia and
Valproate
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